Q99.1

46,XX true hermaphrodite

Coding guidance (WHO 2019)

46,XX with streak gonads 46,XY with streak gonads Pure gonadal dysgenesis

Sibling codes

Q99Other chromosome abnormalities, not elsewhere classified Q99.0Chimera 46,XX/46,XY Q99.2Fragile X chromosome Q99.8Other specified chromosome abnormalities Q99.9Chromosomal abnormality, unspecified